Congenital amyotonia syndrome includes a group of congenital neuromuscular diseases with different causes. As early as 1900, Oppenheim reported a congenital disease in which most muscles had low tension at birth, tendon reflexes disappeared, but there was no electrorheological reaction. At that time, it was considered to be an independent disease. Later, two cases of congenital amyotonia and progressive muscular atrophy of the spinal cord appeared in the same family. It was believed that the pathology of the two diseases was exactly the same, with only slightly different symptoms. There was also an intermediate disease type between the two diseases. Finally, it was generally recognized that the congenital amyotonia described by Oppenheim was a mild form of progressive muscular atrophy of the spinal cord. Benign congenital amyotonia syndrome is congenital myodystony, also known as Oppenheim syndrome, benign congenital myopathy syndrome, etc. This symptom belongs to a more benign type of congenital amyotonia, characterized by weakened tension and muscle weakness in most muscles in infancy after birth.