Glycogen storage disease type VI
Glycogen storage disease VI (GSD-VI) is caused by liver phosphorylase deficiency, mainly liver lesions, and is relatively rare. Children with this disease often present with hepatomegaly and growth retardation in early childhood, with mild hypoglycemia, hyperlipidemia, and increased ketone bodies, and no symptoms of heart and skeletal muscle involvement. With age, hepatomegaly and growth retardation gradually improve, and often disappear during puberty. Most children do not require treatment. To prevent hypoglycemia, they can eat multiple small meals or give themselves a high-carbohydrate diet.
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Site of disease:
whole body -
Infectious :
Not contagious -
Frequent population:
child -
Related symptoms:
Muscle atrophy Enlarged liver Enlarged liver Slow growth Increased transaminase -
Concurrent disease:
Related Drugs
Children like to eat syrup
Manufacturer:
Weifang Tianyang Pharmaceutical Co., Ltd.
Children's Summer Sense Syrup
Manufacturer:
Tai Chi Group Sichuan Nanchong Pharmaceutical Co., Ltd.
Related Ingredients
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Maltitol list
585-88-6 -
Talc list
14807-96-6 -
Sucrose list
57-50-1 -
Costus oil list
8023-88-9